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HMBS Antibody - middle region : FITC
HMBS Antibody - middle region : FITC
Artikelnummer
AVIARP54452_P050FITC
Verpackungseinheit
100μl
Hersteller
Aviva Systems Biology
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Conjugation: FITC: Fluorescein Isothiocyanate
Description of Target: HMBS is a member of the hydroxymethylbilane synthase superfamily. It is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in this gene are associated with the autosomal dominant disease acute intermittent porphyria.This gene encodes a member of the hydroxymethylbilane synthase superfamily. The encoded protein is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in this gene are associated with the autosomal dominant disease acute intermittent porphyria. Alternatively spliced transcript variants encoding different isoforms have been described.
Immunogen: The immunogen is a synthetic peptide directed towards the middle region of human HMBS
Key Reference: Kuo,H.C., J. Neurol. Sci. 260 (1-2), 231-235 (2007)
Molecular Weight: 40kDa
Peptide Sequence: Synthetic peptide located within the following region: SSLRRAAQLQRKFPHLEFRSIRGNLNTRLRKLDEQQEFSAIILATAGLQR
Product Format: Liquid. Purified antibody supplied in 1x PBS buffer.
Protein Name: Porphobilinogen deaminase
Protein Size: 361
Purification: Affinity Purified
Description of Target: HMBS is a member of the hydroxymethylbilane synthase superfamily. It is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in this gene are associated with the autosomal dominant disease acute intermittent porphyria.This gene encodes a member of the hydroxymethylbilane synthase superfamily. The encoded protein is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in this gene are associated with the autosomal dominant disease acute intermittent porphyria. Alternatively spliced transcript variants encoding different isoforms have been described.
Immunogen: The immunogen is a synthetic peptide directed towards the middle region of human HMBS
Key Reference: Kuo,H.C., J. Neurol. Sci. 260 (1-2), 231-235 (2007)
Molecular Weight: 40kDa
Peptide Sequence: Synthetic peptide located within the following region: SSLRRAAQLQRKFPHLEFRSIRGNLNTRLRKLDEQQEFSAIILATAGLQR
Product Format: Liquid. Purified antibody supplied in 1x PBS buffer.
Protein Name: Porphobilinogen deaminase
Protein Size: 361
Purification: Affinity Purified
| Artikelnummer | AVIARP54452_P050FITC |
|---|---|
| Hersteller | Aviva Systems Biology |
| Hersteller Artikelnummer | ARP54452_P050-FITC |
| Green Labware | Nein |
| Verpackungseinheit | 100μl |
| Mengeneinheit | STK |
| Reaktivität | Human, Mouse (Murine), Rat (Rattus), Sheep (Ovine), Rabbit, Dog (Canine), Guinea Pig, Cow (Bovine), Zebrafish, Goat (Caprine), Horse (Equine) |
| Klonalität | Polyclonal |
| Methode | Western Blotting |
| Human Gene ID | 3145 |
| Wirt | Rabbit |
| Produktinformation (PDF) | Download |
| MSDS (PDF) |
|
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Gernot Ensinger, M.Sc.
