ANAG Antibody - N-terminal region : FITC

Conjugation: FITC: Fluorescein Isothiocyanate

Description of Target: This gene encodes an enzyme that degrades heparan sulfate by hydrolysis of terminal N-acetyl-D-glucosamine residues in N-acetyl-alpha-D-glucosaminides. Defects in this gene are the cause of mucopolysaccharidosis type IIIB (MPS-IIIB), also known as Sanfilippo syndrome B. This disease is characterized by the lysosomal accumulation and urinary excretion of heparan sulfate.

Immunogen: The immunogen is a synthetic peptide directed towards the N-terminal region of Human ANAG

Key Reference: N/A

Molecular Weight: 81kDa

Peptide Sequence: Synthetic peptide located within the following region: GVLLLAGAGGAAGDEAREAAAVRALVARLLGPGPAADFSVSVERALAAKP

Product Format: Liquid. Purified antibody supplied in 1x PBS buffer.

Protein Name: Alpha-N-acetylglucosaminidase

Protein Size: 743

Purification: Affinity purified

• Artikelnummer: AVIARP58644_P050FITC
• Hersteller: Aviva Systems Biology
• Hersteller Artikelnummer: ARP58644_P050-FITC
• Green Labware: Nein
• Verpackungseinheit: 100μl
• Mengeneinheit: STK
• Reaktivität: Human, Pig (Porcine), Dog (Canine), Cow (Bovine)
• Klonalität: Polyclonal
• Methode: Western Blotting
• Human Gene ID: 4669
• Wirt: Rabbit