Formulation: A crystalline solid
Formal Name: (R)-3-carboxy-2-(isobutyryloxy)-N,N-dimethyl-N-(methyl-d3)propan-1-aminium, monochloride
Purity: ≥99% deuterated forms (d1-d3)
Formula Markup: C11H19D3NO4 • Cl
Formula Weight: 270,8
Shelf life (days): 730
Notes: Isobutyryl-L-carnitine-d3 is intended for use as an internal standard for the quantification of isobutyryl-L-carnitine by GC- or LC-MS. Isobutyryl-L-carnitine is a natural 4-carbon acylcarnitine that is involved in fatty acid oxidation and organic acid metabolism.{32029} Elevated levels of isobutyryl-L-carnitine are associated with isobutyryl-CoA dehydrogenase deficiency.{32027,32028}