Product Description: 2-Hydroxy-2-methylbutanoic acid, an unusual metabolite, is associated with 2-hydroxyglutaric aciduria and maple syrup urine disease.
Applications: Metabolism-sugar/lipid metabolism
Formula: C5H10O3
References: [1]Dekant W, et al. Biotransformation of MTBE, ETBE, and TAME after inhalation or ingestion in rats and humans. Res Rep Health Eff Inst. 2001 May;(102):29-71; discussion 95-109.
CAS Number: 3739-30-8
Molecular Weight: 118.13
Compound Purity: 98.0
Research Area: Metabolic Disease
Solubility: DMSO : 100 mg/mL (ultrasonic)
Target: Endogenous Metabolite