Formulation: A solid
Purity: ≥95%
Formula Markup: C6H13NO2
Formula Weight: 131,2
Shelf life (days): 1460
CAS Number: 1509-34-8
Notes: L-Alloisoleucine is a branched-chain amino acid and diastereomer of L-isoleucine.{61892} It is formed from L-isoleucine by transamination.{61893} Plasma L-alloisoleucine levels are increased in patients with maple syrup urine disease (MSUD), an inborn error of metabolism characterized by a deficiency in the branched-chain α-ketoacid dehydrogenase complex, the complex that catalyzes the degradation of branched-chain amino acids, leading to the accumulation of branched-chain amino acids in the plasma and urine, a maple syrup-like odor in the urine, and neurological impairments.{61892}