NAGLU Antibody - N-terminal region : HRP

Conjugation: HRP: Horseradish Peroxidase

Description of Target: This gene encodes an enzyme that degrades heparan sulfate by hydrolysis of terminal N-acetyl-D-glucosamine residues in N-acetyl-alpha-D-glucosaminides. Defects in this gene are the cause of mucopolysaccharidosis type IIIB (MPS-IIIB), also known as Sanfilippo syndrome B. This disease is characterized by the lysosomal accumulation and urinary excretion of heparan sulfate.

Immunogen: The immunogen is a synthetic peptide directed towards the N-terminal region of Human NAGLU

Key Reference: N/A

Molecular Weight: 81kDa

Peptide Sequence: Synthetic peptide located within the following region: GVLLLAGAGGAAGDEAREAAAVRALVARLLGPGPAADFSVSVERALAAKP

Product Format: Liquid. Purified antibody is supplied in high phosphate PBS, 100 mm phosphate, 150 mM NaCl, pH 7.6.

Protein Name: Alpha-N-acetylglucosaminidase

Protein Size: 743

Purification: Affinity purified

• SKU: AVIARP58644_P050-HRP
• Manufacturer: Aviva Systems Biology
• Manufacturer SKU: ARP58644_P050-HRP
• Package Unit: 100μl
• Quantity Unit: STK
• Reactivity: Human, Pig (Porcine), Dog (Canine), Cow (Bovine)
• Clonality: Polyclonal
• Application: Western Blotting
• Human Gene ID: 4669
• Host: Rabbit
• Conjugate: Conjugated, HRP