CPS1 Polyclonal Antibody, Rabbit

Abbreviation: CPS1

Target Synonym: CPS1; CPSASE1; PHN; carbamoyl-phosphate synthase 1

Conjugation: Unconjugated

UNIProt ID: P31327

Background: The mitochondrial enzyme encoded by this gene catalyzes synthesis of carbamoyl phosphate from ammonia and bicarbonate. This reaction is the first committed step of the urea cycle, which is important in the removal of excess urea from cells. The encoded protein may also represent a core mitochondrial nucleoid protein. Three transcript variants encoding different isoforms have been found for this gene. The shortest isoform may not be localized to the mitochondrion. Mutations in this gene have been associated with carbamoyl phosphate synthetase deficiency, susceptibility to persistent pulmonary hypertension, and susceptibility to venoocclusive disease after bone marrow transplantation.

Concentration: 1mg/mL

Immunogen: Recombinant fusion protein of human CPS1

Dilution: IF 1:50-1:200

• SKU: ELSE-AB-92349-120
• Manufacturer: Elabscience Biotechnology
• Manufacturer SKU: ELA-E-AB-92349-120
• Green Labware: No
• Package Unit: 120 µl
• Quantity Unit: STK
• Reactivity: Human, Mouse (Murine), Rat (Rattus)
• Clonality: Polyclonal
• Application: Immunofluorescence
• Isotype: IgG
• Host: Rabbit