Product Description: 2-Methylbutyryl-CoA is an intermediate of isoleucine metabolism. 2-Methylbutyryl-CoA dehydrogenase deficiency is a genetic disorder caused by mutations in the HADH2 gene[1].
Formula: C26H44N7O17P3S
References: [1]Goetzman ES, et al. Convergent evolution of a 2-methylbutyryl-CoA dehydrogenase from isovaleryl-CoA dehydrogenase in Solanum tuberosum. J Biol Chem. 2005 Feb 11;280(6):4873-9.