Formulation: A solid
Formal Name: 3-methyl-2-pentenedioic acid
Purity: ≥95% (mixture of E/Z isomers)
Formula Markup: C6H8O4
Formula Weight: 144,1
Shelf life (days): 1460
CAS Number: 5746-90-7
Notes: 3-Methylglutaconic acid (3-MGA) is a branched-chain organic acid and product of leucine catabolism.{62255} 3-MGA accumulates in 3-methylglutaconic aciduria, which is caused by an inborn error of leucine metabolism characterized by 3-MGA-CoA hydratase deficiency, leading to delayed development, hypoglycemia, metabolic acidosis, and neurological impairments.{58551,62255}