Product Description: H-Abu-OH, one of the three isomers of aminobutyric acid, is elevated in the plasma of children with with Reye's syndrome, tyrosinemia, homocystinuria, nonketotic hyperglycinemia, and ornithine transcarbamylase deficiency.
Applications: Metabolism-protein/nucleotide metabolism
Formula: C4H9NO2
References: [1]Yudkoff M, et al. On the clinical significance of the plasma alpha-amino-n-butyric acid:leucine ratio. Am J Clin Nutr. 1979 Feb;32(2):282-5.
CAS Number: 1492-24-6
Molecular Weight: 103.12
Compound Purity: 98.0
Research Area: Metabolic Disease
Solubility: H2O : 50 mg/mL (ultrasonic)
Target: Endogenous Metabolite